Background: ebstein’s anomaly is a rare and complex heart defect that affects the tricuspid valve and is accountable for around 1% ofcongenital cardiac abnormalities. It is one of the most common congenital causes of tricuspid valve regurgitation. ebstein’s anomalyoften is diagnosed prenatally, due to its severe cardiomegaly. some individuals with this anomaly do not experience complicationsuntil adulthood and even then, they have mostly minor complaints like exercise intolerance. an atrial septal defect is most commonly(70-90%) associated with ebstein’s anomaly. However, ventricular septal defect (VsD) can be associated with 2-6% of the cases.Case presentation: this report presents a case of surgical intervention for a 38-year-old female with ebstein’s anomaly symptomaticwith moderate-severe pulmonary regurgitation and foramen ovale apertum.Conclusions: ebstein anomaly is a complicated form of congenital heart disease with variable clinical presentations. the anestheticplan must also focus on maintenance of rV function and avoidance of increase in pVr. reversible causes of increased pVr, such asacidemia, hypoxemia, and hypercarbia must be avoided. Agents that lower PVR, such as nitrates, and nitric oxide may be beneficialin patients with severe pulmonary hypertension.With a sound knowledge of the cardiac anatomy, accurate scheming of surgical outcomes, routine follow-ups, multidisciplinary teamapproach, and better management, an experienced center can ultimately improve the prognosis of such patients (PDF) Perioperative Management for Surgical Repair of Ebstein's Anomaly. A Case Report. Available from: https://www.researchgate.net/publication/353752308_Perioperative_Management_for_Surgical_Repair_of_Ebstein's_Anomaly_A_Case_Report [accessed Jun 04 2024].
Perioperative Management for Surgical Repair of Ebstein's Anomaly. A Case Report
Jacob Zeitani
2021
Abstract
Background: ebstein’s anomaly is a rare and complex heart defect that affects the tricuspid valve and is accountable for around 1% ofcongenital cardiac abnormalities. It is one of the most common congenital causes of tricuspid valve regurgitation. ebstein’s anomalyoften is diagnosed prenatally, due to its severe cardiomegaly. some individuals with this anomaly do not experience complicationsuntil adulthood and even then, they have mostly minor complaints like exercise intolerance. an atrial septal defect is most commonly(70-90%) associated with ebstein’s anomaly. However, ventricular septal defect (VsD) can be associated with 2-6% of the cases.Case presentation: this report presents a case of surgical intervention for a 38-year-old female with ebstein’s anomaly symptomaticwith moderate-severe pulmonary regurgitation and foramen ovale apertum.Conclusions: ebstein anomaly is a complicated form of congenital heart disease with variable clinical presentations. the anestheticplan must also focus on maintenance of rV function and avoidance of increase in pVr. reversible causes of increased pVr, such asacidemia, hypoxemia, and hypercarbia must be avoided. Agents that lower PVR, such as nitrates, and nitric oxide may be beneficialin patients with severe pulmonary hypertension.With a sound knowledge of the cardiac anatomy, accurate scheming of surgical outcomes, routine follow-ups, multidisciplinary teamapproach, and better management, an experienced center can ultimately improve the prognosis of such patients (PDF) Perioperative Management for Surgical Repair of Ebstein's Anomaly. A Case Report. Available from: https://www.researchgate.net/publication/353752308_Perioperative_Management_for_Surgical_Repair_of_Ebstein's_Anomaly_A_Case_Report [accessed Jun 04 2024].I documenti in SFERA sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
