Adult onset Still's disease (AOSD) is a rare systemic inflammatory disease of unknown etiology characterized by four cardinal signs which are almost always present in patients: high spiking fever, arthralgia (with or without synovitis), maculo-papular salmon-pink evanescent skin rash, striking leukocytosis with neutrophilia. Here, we review the clinical features of AOSD and describe the best practice approaches for its management, reviewing available guidelines and recommendations and providing experts' insights.
Data di pubblicazione: | 2017 | |
Titolo: | How I treat patients with adult onset Still's disease in clinical practice | |
Autori: | Govoni, Marcello; Bortoluzzi, Alessandra; Rossi, Daniela; Modena, Vittorio | |
Rivista: | AUTOIMMUNITY REVIEWS | |
Keywords: | Adult; Humans; Still's Disease, Adult-Onset | |
Abstract in inglese: | Adult onset Still's disease (AOSD) is a rare systemic inflammatory disease of unknown etiology characterized by four cardinal signs which are almost always present in patients: high spiking fever, arthralgia (with or without synovitis), maculo-papular salmon-pink evanescent skin rash, striking leukocytosis with neutrophilia. Here, we review the clinical features of AOSD and describe the best practice approaches for its management, reviewing available guidelines and recommendations and providing experts' insights. | |
Digital Object Identifier (DOI): | 10.1016/j.autrev.2017.07.017 | |
Handle: | http://hdl.handle.net/11392/2374119 | |
Appare nelle tipologie: | 03.1 Articolo su rivista |
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AOSD how I treat - Autoimmun Rev 2017.pdf | Post print | Post-print | ![]() | Open Access Visualizza/Apri |
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