Erdheim-Chester disease is an idiopathic condition characterized by a xanthogranulomatous process infiltrating the bones, lungs, heart, retroperitoneum and other tissues. This condition is often fatal. Ocular findings are rare. The authors report a case of bilateral xanthelasmas and bilateral massive orbital infiltration in a 61-year-old man with severe retroperitoneal fibrosis, renal and cardiovascular problems. The ophthalmic manifestations and differential diagnosis of this peculiar pathologic condition are discussed.

Bilateral orbital involvement in Erdheim-Chester disease

DE PALMA, Paolo;ROSSI, Antonio;MARZOLA, Andrea;
1998

Abstract

Erdheim-Chester disease is an idiopathic condition characterized by a xanthogranulomatous process infiltrating the bones, lungs, heart, retroperitoneum and other tissues. This condition is often fatal. Ocular findings are rare. The authors report a case of bilateral xanthelasmas and bilateral massive orbital infiltration in a 61-year-old man with severe retroperitoneal fibrosis, renal and cardiovascular problems. The ophthalmic manifestations and differential diagnosis of this peculiar pathologic condition are discussed.
1998
DE PALMA, Paolo; Ravalli, L.; Grisanti, F.; Rossi, Antonio; Marzola, Andrea; Nielsen, I.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11392/1205957
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